MACRODYSTROPHIA LIPOMATOSA: A RARE ENTITY WITH CHARACTERISTIC RADIOLOGICAL FINDINGS
نویسندگان
چکیده
منابع مشابه
Macrodystrophia Lipomatosa: A rare presentation
Macrodystrophia lipomatosa is a rare congenital nonhereditary mesenchymal hamartomatous malformation resulting in localized gigantism of parts of extremities that manifests clinically as macrodactyly or megalodactyly. Radiological and Pathological hallmark is the disproportionate fibroadipose tissue proliferation in subcutaneous tissue, nerve sheaths, and periosteum that leads to soft tissue an...
متن کاملMacrodystrophia Lipomatosa: Clinico-patho-radiological Correlation
Macrodystrophia lipomatosa is a rare congenital nonhereditary developmental anomaly. It is characterized by hamartomatous proliferation of the soft tissue leading to disproportionate enlargement of the limbs and digits. Since it leads to diagnostic dilemma, it has to be differentiated from various other conditions as they differ in course, prognosis, complications, and treatment. Herein, we pre...
متن کاملMacrodystrophia Lipomatosa
remaining three ulnar digits appeared normal. Magnetic resonance imaging (MRI) revealed characteristics of macrodystrophia lipomatosa such as enlargement and marked proliferation of the adipose tissues of the left hand, especially the radial aspect. MRI also demonstrated excessive fibrofatty tissue around the affected digits. This tissue has the same signal characteristics as fat on MRI, that i...
متن کاملMACRODYSTROPHIA LIPOMATOSA: CT AND M R FINDINGS
Macrodystrophia lipomatosa is a rare congenital form of localized gigantism characterized by an increase in all mesenchymal elements, particularly fibroadipose tissue. MR imaging can be used to examine the soft tissue and detect the fibrous and fatty hypertrophy that characterizes this condition and also diagnose an associated fibrolipomatous hamartoma of the median or plantar nerve. We des...
متن کاملMacrodystrophia lipomatosa: four case reports
AIM Macrodystrophia lipomatosa is a rare cause of gigantism of limb which can be confused with other common causes like congenital lymphedema. It presents usually with loss of function and cosmetic problems. Four cases are described with emphasis on clinical presentation, differential diagnoses, imaging and treatment options. METHODS & RESULTS Four patients of macrodystrophia lipomatosa were ...
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ژورنال
عنوان ژورنال: Volume 5, Issue 1, Jan - Feb 2019
سال: 2019
ISSN: 2454-1303,2454-129X
DOI: 10.32677/ijcr.2019.v05.i01.031